Miranda Sandra Maria Bitencourt, de Miranda João Nestor Rodrigues, de Souza Filho João Basílio
Santa Casa de Misericórdia Medical School, Federal University and Clinical Hospital, Santa Luzia, Brazil.
Int J Dermatol. 2004 Dec;43(12):913-4. doi: 10.1111/j.1365-4632.2004.02315.x.
Porokeratosis is a rare group of keratinizing diseases. It is inherited as an autosomal dominant disease with variable penetrance, although sporadic cases are often reported. Porokeratosis has as its histological hallmark the typical cornoid lamella. Porokeratosis lesions localized on the face can vary from superficial to destructive in nature. Only 12 cases have been reported in the literature to date. We report one more unusual case of destructive facial porokeratosis.
汗孔角化症是一组罕见的角化性疾病。它作为一种常染色体显性疾病遗传，具有可变的外显率，尽管经常有散发病例的报道。汗孔角化症的组织学特征是典型的鸡眼样板层。面部局限性汗孔角化症病变的性质可从浅表性到破坏性不等。迄今为止，文献中仅报道了12例。我们报告了1例更罕见的面部破坏性汗孔角化症病例。
