Tjalma W A A, Colpaert C G A
Department of Gynecology, Gynecologic Oncology, University Hospital Antwerp, Wilrijkstraat 10, 2650 Edegem, Belgium.
Gynecol Oncol. 2005 Feb;96(2):548-51. doi: 10.1016/j.ygyno.2004.10.013.
Myxoid leiomyosarcoma (MLMS) of the vulva is a mesenchymal tumor with only five reported cases in the literature.
We report an 85-year-old woman with a unilateral nonulcerating, painless vulvar mass. According to the patient, the mass slowly enlarged. Initial biopsies were benign. However, clinically, this lesion was suspicious for a soft tissue tumor. Therefore, the mass was removed by a wide local excision. Definitive histology revealed a myxoid leiomyosarcoma of the vulva. At present, 25 months after the operation, the patient is well with no sign of recurrence.
Vulvar myxoid leiomyosarcomas are rare and can be confused with other benign or malignant tumors. It is important to be aware of this rare tumor variant, in order to plan appropriate treatment.
外阴黏液样平滑肌肉瘤(MLMS)是一种间叶性肿瘤,文献中仅报道过5例。
我们报告一名85岁女性,其单侧外阴出现非溃疡性、无痛性肿块。据患者称,肿块缓慢增大。最初的活检结果为良性。然而,临床上该病变怀疑是软组织肿瘤。因此,通过广泛局部切除将肿块切除。最终组织学检查显示为外阴黏液样平滑肌肉瘤。目前,术后25个月,患者情况良好,无复发迹象。
外阴黏液样平滑肌肉瘤罕见,可与其他良性或恶性肿瘤相混淆。认识到这种罕见的肿瘤变体对于制定合适的治疗方案很重要。