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勒米特-迪克洛病(发育异常性小脑神经节细胞瘤)。

Lhermitte-Duclos disease (dysplastic cerebellar gangliocytoma).

作者信息

Rafique Muhammad Zafar

机构信息

Department of Radiology, Aga Khan University Hospital, Karachi.

出版信息

J Coll Physicians Surg Pak. 2005 Jan;15(1):48-9.

Abstract

This case report describes an adult male presenting with ataxia. Dysplastic cerebellar gangliocytoma, the Lhermitte-Duclos disease, was diagnosed on neuroimaging. Diagnosis was confirmed on histopathology of surgically removed lesion. Patient underwent an uneventful recovery following operative treatment.

摘要

本病例报告描述了一名出现共济失调的成年男性。神经影像学诊断为发育异常性小脑神经节细胞瘤,即Lhermitte-Duclos病。手术切除病变的组织病理学检查证实了诊断。患者接受手术治疗后顺利康复。

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