van Dijk Nynke, Immink Rogier V, Mulder Barbara J M, van Lieshout Johannes J, Wieling Wouter
Department of Internal Medicine F4-222, Academic Medical Center, Meibergdreef 9, 1105 AZ Amsterdam, The Netherlands.
Europace. 2005 Jan;7(1):25-7. doi: 10.1016/j.eupc.2004.05.009.
A 33-year old male patient, with Marfan's syndrome, reported symptoms of orthostatic intolerance and fatigue as a longstanding problem. Orthostatic cardiovascular examination showed poor orthostatic tolerance, with a rise in heart rate and a fall in arterial blood pressure and cerebral blood flow velocity. Self-discovered physical counterpressure manoeuvers improved symptoms, related to a substantial increase in arterial pressure and cerebral perfusion. When orthostatic complaint are reported by patients with Marfan's syndrome, physical counterpressure manoeuvers should be advised to reduce symptoms of postural hypotension.
一名33岁患有马凡氏综合征的男性患者，长期存在体位性不耐受和疲劳症状。体位性心血管检查显示体位耐受性差，心率上升，动脉血压和脑血流速度下降。自我发现的身体对抗压力动作可改善症状，这与动脉压和脑灌注的显著增加有关。当马凡氏综合征患者报告有体位性不适时，建议采用身体对抗压力动作来减轻体位性低血压症状。
