未折叠蛋白反应传感器IRE1α在B细胞淋巴细胞生成的两个不同步骤中是必需的。
The unfolded protein response sensor IRE1alpha is required at 2 distinct steps in B cell lymphopoiesis.
作者信息
Zhang Kezhong, Wong Hetty N, Song Benbo, Miller Corey N, Scheuner Donalyn, Kaufman Randal J
机构信息
Department of Biological Chemistry and Howard Hughes Medical Institute, University of Michigan Medical Center, Ann Arbor, Michigan 48109, USA.
出版信息
J Clin Invest. 2005 Feb;115(2):268-81. doi: 10.1172/JCI21848.
B lymphocyte differentiation is coordinated with the induction of high-level Ig secretion and expansion of the secretory pathway. Upon accumulation of unfolded proteins in the lumen of the ER, cells activate an intracellular signaling pathway termed the unfolded protein response (UPR). Two major proximal sensors of the UPR are inositol-requiring enzyme 1alpha (IRE1alpha), an ER transmembrane protein kinase/endoribonuclease, and ER-resident eukaryotic translation initiation factor 2alpha (eIF2alpha) kinase (PERK). To elucidate whether the UPR plays an important role in lymphopoiesis, we carried out reconstitution of recombinase-activating gene 2-deficient (rag2-/-) mice with hematopoietic cells defective in either IRE1alpha- or PERK-mediated signaling. IRE1alpha-deficient (ire1alpha-/-) HSCs can proliferate and give rise to pro-B cells that home to bone marrow. However, IRE1alpha, but not its catalytic activities, is required for Ig gene rearrangement and production of B cell receptors (BCRs). Analysis of rag2-/- mice transplanted with IRE1alpha trans-dominant-negative bone marrow cells demonstrated an additional requirement for IRE1alpha in B lymphopoiesis: both the IRE1alpha kinase and RNase catalytic activities are required to splice the mRNA encoding X-box-binding protein 1 (XBP1) for terminal differentiation of mature B cells into antibody-secreting plasma cells. Furthermore, UPR-mediated translational control through eIF2alpha phosphorylation is not required for B lymphocyte maturation and/or plasma cell differentiation. These results suggest specific requirements of the IRE1alpha-mediated UPR subpathway in the early and late stages of B lymphopoiesis.
B淋巴细胞分化与高水平Ig分泌的诱导以及分泌途径的扩展相协调。当内质网腔中未折叠蛋白积累时,细胞会激活一种称为未折叠蛋白反应(UPR)的细胞内信号通路。UPR的两个主要近端传感器是肌醇需求酶1α(IRE1α),一种内质网跨膜蛋白激酶/核糖核酸酶,以及内质网驻留真核翻译起始因子2α(eIF2α)激酶(PERK)。为了阐明UPR在淋巴细胞生成中是否起重要作用,我们用在IRE1α或PERK介导的信号传导方面有缺陷的造血细胞对重组激活基因2缺陷(rag2-/-)小鼠进行了重建。缺乏IRE1α(ire1α-/-)的造血干细胞可以增殖并产生归巢到骨髓的前B细胞。然而,Ig基因重排和B细胞受体(BCR)的产生需要IRE1α,而不是其催化活性。对移植了IRE1α反式显性负性骨髓细胞的rag2-/-小鼠的分析表明,B淋巴细胞生成中对IRE1α还有额外需求:IRE1α激酶和核糖核酸酶催化活性都需要剪接编码X盒结合蛋白1(XBP1)的mRNA,以使成熟B细胞终末分化为分泌抗体的浆细胞。此外,通过eIF2α磷酸化的UPR介导的翻译控制对于B淋巴细胞成熟和/或浆细胞分化不是必需的。这些结果表明IRE1α介导的UPR子途径在B淋巴细胞生成的早期和晚期有特定需求。