Tamiolakis D, Arvanitidou V, Nikolaidou S, Barbagadaki S, Avgidou K, Boglou P, Papadopoulos N
Department of Cytopathology, General Hospital of Chania, Crete, Greece.
Minerva Gastroenterol Dietol. 2004 Jun;50(2):179-81.
Personal experience in the treatment of a female patient presenting a pure monolobar Caroli's disease, is described. The woman was asymptomatic so far; during the last 2 weeks she was admitted on 3 occasions with repeated attacks of cholangitis and obstructive jaundice. Surgery was performed for relief of the jaundice. A diagnosis of segmental Caroli's disease (congenital dilatation of intrahepatic bile ducts) with congenital fibrosis was made on the basis of marked fibrous septa with the characteristic ductal plate formation on left hepatectomy specimen and the cysts seen on ultrasound.
本文描述了一位患有单纯单叶型卡罗里病女性患者的治疗经历。该女性此前无症状；在过去两周内，她因胆管炎和梗阻性黄疸反复发作三次入院。为缓解黄疸症状进行了手术。根据左肝切除标本中明显的纤维间隔、典型的导管板形成以及超声检查发现的囊肿，诊断为节段性卡罗里病（肝内胆管先天性扩张）合并先天性肝纤维化。
