一例 Darier-White 病并发卡波西水痘样疹。

A case of Kaposi varicelliform eruption in Darier-White disease.

作者信息

Donnelly Alyssa A, Butler Robert, Miller Charles H

机构信息

Branch Medical Clinic Everett, Washington, USA.

出版信息

Cutis. 2005 Jan;75(1):33-6.

PMID:15732432

Abstract

Darier-White disease (DWD), otherwise known as keratosis follicularis, is a rare disorder of keratinization of the epidermis, mucous membranes, and nails. It is autosomal dominant in transmission. Patients with DWD are prone to frequent superinfection including the rare complication of Kaposi varicelliform eruption. It is postulated that a defect in cell-mediated immunity may contribute to this predisposition.

摘要

达里埃-怀特病（DWD），又称毛囊角化病，是一种罕见的表皮、黏膜和指甲角化异常疾病。其遗传方式为常染色体显性遗传。DWD患者容易频繁发生继发感染，包括罕见的卡波西水痘样疹并发症。据推测，细胞介导免疫缺陷可能是导致这种易感性的原因。