Crovetto de la Torre M A, Whyte Orozco J, Cisneros Gimeno A I, Basurko Aboitz J M, Oleaga Zufiria L, Sarrat Torreguitart R
Servicios de Otorrinolaringología y Radiología, Hospital de Basurto, Bilbao.
Acta Otorrinolaringol Esp. 2005 Jan;56(1):6-11. doi: 10.1016/s0001-6519(05)78562-9.
Presenting the first case of superior semicircular canal dehiscence syndrome in the Spanish literature and to establish, using embryological studies, the period in wich superior semicircular canal dehiscence originates.
52 embryos and foetuses, from 6 mm to foetal maturity, were studied. The case of a patient suffering from superior semicircular canal dehiscence syndrome is presented.
The superior semicircular canal and the intracranial space are communicated through bony lacunae, in the period between the 24th and 28th week of foetal development, but this communication is discontinued in the 30th week. Permeability of these lacunae, later in life, could result in the development of superior semicircular canal dehiscence syndrome. The clinical results of the surgical repair of this abnormal communication, in this particular case, using a middle fossa approach and a transmastoid approach is presented.
Superior Semicircular Canal Dehiscence Syndrome could be due to an abnormality in foetal development and its genesis, therefore, could be prenatal. Surgical repair via transmastoid approach is a reasonable alternative treatment to the middle fossa approach.
介绍西班牙文献中首例上半规管裂综合征病例，并通过胚胎学研究确定上半规管裂发生的时期。
研究了52例从6毫米至胎儿成熟的胚胎和胎儿。报告了1例患有上半规管裂综合征的患者病例。
在胎儿发育的第24至28周期间，上半规管与颅内空间通过骨腔隙相通，但这种相通在第30周时中断。这些腔隙在后期的通透性可能导致上半规管裂综合征的发生。介绍了在该特定病例中，采用中颅窝入路和经乳突入路对这种异常相通进行手术修复的临床结果。
上半规管裂综合征可能归因于胎儿发育异常，其起源可能为产前。经乳突入路手术修复是中颅窝入路的一种合理替代治疗方法。
