淋巴管平滑肌瘤病合并巨大肺大疱：1例报告

Lymphangioleiomyomatosis with a giant bulla: report of a case.

作者信息

Fujiwara Taiki, Iyoda Akira, Hiroshima Kenzo, Yusa Toshikazu, Igarashi Natsuhiko, Tatsumi Koichiro, Otsuji Mizuto, Sekine Yasuo, Shibuya Kiyoshi, Iizasa Toshihiko, Saitoh Yukio, Fujisawa Takehiko

机构信息

Department of Thoracic Surgery, Graduate School of Medicine, Chiba University, 1-8-1 Inohana, Chuo-ku, Chiba 260-8670, Japan.

出版信息

Surg Today. 2005;35(3):247-9. doi: 10.1007/s00595-004-2903-5.

DOI:10.1007/s00595-004-2903-5

PMID:15772798

Abstract

We report a case of lymphangioleiomyomatosis (LAM) with a giant bulla. A 33-year-old woman was referred to our department for treatment of dyspnea. Chest computed tomography showed a giant bulla with many smaller bullae. To obtain a definitive diagnosis and relieve the dyspnea, we performed a lung biopsy and bullectomy, after which her symptoms and pulmonary function improved remarkably. She was commenced on progesterone, which improved her condition even further. This case report retrospectively follows the progression of her disease from the onset of symptoms 5 years before she was referred to us for treatment.

摘要

我们报告一例患有巨大肺大疱的淋巴管平滑肌瘤病（LAM）病例。一名33岁女性因呼吸困难前来我院就诊。胸部计算机断层扫描显示一个巨大肺大疱以及许多较小的肺大疱。为明确诊断并缓解呼吸困难，我们进行了肺活检和肺大疱切除术，术后她的症状和肺功能显著改善。我们让她开始使用孕酮治疗，这使她的病情进一步好转。本病例报告回顾了她从出现症状到前来我院治疗前5年期间疾病的进展情况。