Unit for Interstitial Lung Diseases, Department of Respiratory Medicine, University Hospital Leuven, Leuven, Belgium.
Thorax. 2013 Jan;68(1):111-3. doi: 10.1136/thoraxjnl-2012-201973. Epub 2012 Aug 3.
We present a case of a 32-year-old woman who was diagnosed with lymphangioleiomyomatosis (LAM) after detecting a mass in the upper anterior mediastinum. Two years after presentation another metastatic localisation of LAM occurred in the cervical region. With this article we would like to highlight the fact that there are still a lot of unanswered questions, especially regarding the best management of extrapulmonary LAM.
我们报告了 1 例 32 岁女性病例，该患者在前纵隔上部发现肿块后被诊断为淋巴管平滑肌瘤病（LAM）。就诊 2 年后，LAM 又在颈部出现了另一个转移病灶。本文旨在强调目前仍有许多悬而未决的问题，特别是在外周性 LAM 的最佳治疗管理方面。
