Kikuchi Seiya, Yokozawa Masato
Department of Cardiovascular Surgery, Hokkaido Children's Hospital and Medical Center, Hokkaido, Japan.
Ann Thorac Cardiovasc Surg. 2005 Feb;11(1):44-7.
A male infant with an extremely rare combination of absent pulmonary valve, tetralogy of Fallot and atrioventricular septal defect presented without symptoms of respiratory distress or congestive heart failure. He underwent successful primary repair at the age of 5 months. The procedure consisted of double-patch repair of the atrioventricular septal defect and right ventricular outflow tract reconstruction with a monocusp transannular patch. Resection or plication of a dilated pulmonary artery was not required. The patient is doing well without any symptoms 5 years after repair.
一名患有肺动脉瓣缺如、法洛四联症和房室间隔缺损这一极其罕见组合的男婴，在无呼吸窘迫或充血性心力衰竭症状的情况下就诊。他在5个月大时接受了成功的一期修复手术。手术包括房室间隔缺损的双补片修复以及使用单叶瓣跨环补片进行右心室流出道重建。无需切除或折叠扩张的肺动脉。修复术后5年，患者情况良好，没有任何症状。
