Tatebe Shoh, Asami Fuyuki, Shinohara Hirohiko, Okamoto Takeshi, Kuraoka Setsuo
Department of Thoracic and Cardiovascular Surgery, Mito Saiseikai General Hospital, Mito, Japan.
Circ J. 2005 Apr;69(4):503-6. doi: 10.1253/circj.69.503.
A vascular manifestation of von Recklinghausen's disease is rare, but may be fatal if it is disrupted. A 39-year-old male with von Recklinghausen's disease presented with a large and tender bruise extending from his left neck to his left shoulder and arm. Computerized axial tomography revealed a ruptured aneurysm of the left subclavian artery. The patient underwent emergency surgery to exclude the aneurysm, and cross-over bypass grafting of both subclavian arteries was performed. We present a brief review of vascular maintestation of von Recklinghausen's disease, as well as a discussion regarding the strategy for treating this rare presentation.
冯·雷克林霍增氏病的血管表现较为罕见,但一旦破裂可能会致命。一名患有冯·雷克林霍增氏病的39岁男性,出现了一个从左颈部延伸至左肩及手臂的巨大且触痛的瘀斑。计算机断层扫描显示左锁骨下动脉动脉瘤破裂。患者接受了紧急手术以切除动脉瘤,并对双侧锁骨下动脉进行了交叉搭桥移植术。我们简要回顾了冯·雷克林霍增氏病的血管表现,并讨论了针对这种罕见表现的治疗策略。