Apoznański W, Sawicz-Birkowska K, Pietras W, Dorobisz U, Szydełko T
Department of Paediatric Surgery and Urology, University of Medicine, Wrocław, Poland.
Eur J Pediatr Surg. 2005 Feb;15(1):53-5. doi: 10.1055/s-2004-830553.
Nephroblastoma is one of the most common solid tumours in children. It also is the most frequent tumour found in the kidneys. In 5 % of cases it affects both kidneys at the same time. About 70 - 80 new cases of Wilms tumour are registered in Poland annually, usually in patients aged from 1 to 7 years. Extrarenal Wilms tumours are extremely rare. Due to its rarity, series with more cases are based upon material collected from many clinical centers.
We would like to present a case of a boy in whom we diagnosed nephroblastoma in the retroperitoneal space 14 years after he had completed a complex therapy for bilateral Wilms tumour.
The development of an extrarenal tumour 14 years after complex treatment for bilateral nephroblastoma is related to the survival of metanephros located outside the kidney.