Morandi A, Fagnani A M, Runza L, Farris G, Zanini A, Parolini F, Bassi G, Gentilino V, Macchini F, Arnoldi R, Leva E
Department of Pediatric Surgery, FONDAZIONE IRCCS Ca' Granda Ospedale Maggiore Policlinico, Via Commenda 10, 20122 Milano, Italy.
Pediatr Surg Int. 2013 Sep;29(9):961-4. doi: 10.1007/s00383-013-3338-0. Epub 2013 Jun 22.
We report an extremely rare case of extrarenal testicular Wilms' tumor in a 3-year-old boy with intrabdominal undescended left testis. The patient was admitted because of pain and vomiting, with evidence of a huge abdominal mass. At surgery a large tumor arising from the intrabdominal testis was found. Histology showed the classical triphasic Wilms' tumor elements: epithelial, mesenchymal and blastemal areas. Extrarenal Wilms' tumors account for only 3% of all Wilms' tumors and just -100 cases have been reported in literature. Testicular origin is anecdotic. We present histomorphological, histogenetic, clinical, diagnostic, prognostic and therapeutic features of this rare tumor.
我们报告了一例极为罕见的肾外睾丸威尔姆斯瘤，患者为一名3岁男孩，其左侧睾丸未降入阴囊而位于腹腔内。该患者因疼痛和呕吐入院，检查发现腹部有巨大肿块。手术中发现一个源于腹腔内睾丸的大肿瘤。组织学检查显示出经典的三相威尔姆斯瘤成分：上皮、间充质和胚基区域。肾外威尔姆斯瘤仅占所有威尔姆斯瘤的3%，文献中仅报道了约100例。睾丸起源的情况较为罕见。我们展示了这种罕见肿瘤的组织形态学、组织发生学、临床、诊断、预后及治疗特征。
