León Francisco, Sánchez Laura, Camarero Cristina, Roy Garbiñe
Departments of Immunology and Paediatrics, Hospital Ramón y Cajal, Madrid, Spain.
Dig Dis Sci. 2005 Mar;50(3):593-600. doi: 10.1007/s10620-005-2480-5.
One of the earliest signs of mucosal immune activation in celiac disease (CD) is an increase in the intraepithelial lymphocyte (IEL) count in the small intestinal epithelium. Though most of those IELs express T cell receptor (TcR)-alphabeta chains, CD is characterized by an increase in TcR-gammadelta+ IELs and by the loss of CD3- IELs. There is currently little evidence that these changes in IEL subset distribution are of relevance in the pathogenesis of CD. We aimed to determine the pattern of cytokine production by IEL subsets isolated from duodenal biopsy specimens from control subjects and CD patients at different stages of the disease. We quantified the capacity of IEL subsets to produce IFN-gamma, TNF-alpha, IL-2, IL-4, and IL-10 by intracellular staining by flow cytometry. All IEL subsets studied displayed a type I cytokine profile in both CD and control subjects, with TcR-alphabeta+ IELs being the main IFN-y producers. Untreated CD exhibited a trend toward a superior accumulation of IFN-gamma per cell but a reduced proportion of INF-gamma+ cells in vitro in association with a significantly increased apoptotic rate of IELs. IL-4 was almost undetectable in all cases and IL-10 showed a tendency to increase in treated and "silent" celiac patients. IEL subsets have a similar Th1 profile in controls and CD patients, and the superior in vitro apoptosis of IELs from CD patients may reflect their superior in vivo activation. The induction of IL-10-dependent regulatory Tr1 responses may be of potential clinical significance in this disease and merits further investigation.
乳糜泻(CD)黏膜免疫激活的最早迹象之一是小肠上皮内上皮淋巴细胞(IEL)数量增加。尽管这些IEL中的大多数表达T细胞受体(TcR)αβ链,但CD的特征是TcRγδ⁺ IEL增加以及CD3⁻ IEL缺失。目前几乎没有证据表明IEL亚群分布的这些变化与CD的发病机制相关。我们旨在确定从疾病不同阶段的对照受试者和CD患者的十二指肠活检标本中分离出的IEL亚群产生细胞因子的模式。我们通过流式细胞术细胞内染色定量了IEL亚群产生干扰素-γ(IFN-γ)、肿瘤坏死因子-α(TNF-α)、白细胞介素-2(IL-2)、白细胞介素-4(IL-4)和白细胞介素-10(IL-10)的能力。在CD患者和对照受试者中,所有研究的IEL亚群均显示出I型细胞因子谱,其中TcRαβ⁺ IEL是主要的IFN-γ产生者。未经治疗的CD在体外显示出每个细胞IFN-γ积累增加的趋势,但IFN-γ⁺细胞比例降低,同时IEL的凋亡率显著增加。在所有病例中几乎检测不到IL-4,在接受治疗的和“无症状”乳糜泻患者中,IL-10有增加的趋势。对照受试者和CD患者的IEL亚群具有相似的Th1谱,CD患者IEL在体外更高的凋亡率可能反映了它们在体内更高的激活状态。IL-10依赖性调节性Tr1反应的诱导在这种疾病中可能具有潜在的临床意义,值得进一步研究。