磁共振成像在无杜安眼球后退综合征特征性临床表现儿童中的应用价值
Usefulness of MR imaging in children without characteristic clinical findings of Duane's retraction syndrome.
作者信息
Kim Jae Hyoung, Hwang Jeong-Min
机构信息
Department of Radiology, Seoul National University College of Medicine, Seoul National University Bundang Hospital, Gumi-dong, Bundang-gu, Sungnam-si, Korea.
出版信息
AJNR Am J Neuroradiol. 2005 Apr;26(4):702-5.
BACKGROUND AND PURPOSE
Duane's retraction syndrome (DRS) consists of a congenital abduction deficit of the eyeball accompanied by retraction of the globe on attempted adduction and by upshoots or downshoots of the affected eye on adduction. These characteristic diagnostic signs of DRS, however, might not be manifested in early childhood. We evaluated the usefulness of MR imaging as a diagnostic tool in such cases.
METHODS
Thin-section gradient-echo imaging at the brain stem level was performed in two pediatric patients with only abduction deficit and 10 control children. Imaging findings were analyzed focused on the presence or absence of the abducens nerve.
RESULTS
The abducens nerve on the affected side was absent in three of three affected eyes in two patients. The right and left abducens nerves were well identified in all 10 control subjects.
CONCLUSION
MR imaging is useful for the differential diagnosis of abduction deficit of the eyeball in pediatric patients. The absence of the abducens nerve suggests DRS strongly in children with abduction deficit.
背景与目的
杜安眼球后退综合征（DRS）表现为先天性眼球外展功能障碍，试图内收眼球时眼球后退，并伴有患眼内收时上转或下转。然而，DRS这些典型的诊断体征在儿童早期可能并不明显。我们评估了磁共振成像（MR成像）在此类病例中作为诊断工具的实用性。
方法
对两名仅有外展功能障碍的儿科患者及10名对照儿童进行脑干水平的薄层梯度回波成像。重点分析成像结果中展神经的有无。
结果
两名患者的三只患眼中，有三只患侧展神经缺失。10名对照受试者的左右展神经均清晰可见。
结论
MR成像有助于小儿眼球外展功能障碍的鉴别诊断。展神经缺失强烈提示外展功能障碍儿童患有DRS。
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