George Christopher H, Yin Chang Cheng, Lai F Anthony
Wales Heart Research Institute, Department of Cardiology, College of Medicine, Cardiff University, UK CF14 4XN.
Cell Biochem Biophys. 2005;42(2):197-222. doi: 10.1385/CBB:42:2:197.
Identification of the genetic basis of human diseases linked to dysfunctional free calcium (Ca2+) signaling has triggered an explosion of interest in the functional characterization of the molecular components regulating intracellular Ca2+ homeostasis. There is a growing appreciation of the central role of intracellular ryanodine-sensitive Ca2+ release channel (RyR) regulation in skeletal and cardiac muscle pathologies, including malignant hyperthermia, heart failure, and sudden cardiac death. The use of cloned RyR isoforms and recombinant expression techniques has greatly facilitated the elucidation of the molecular basis of RyR Ca2+ release functionality. This review will focus on the recombinant techniques used in the functional characterization of recombinant RyR isoforms and the insights that these approaches have yielded in unraveling the mechanistic basis of RyR channel functionality.
与游离钙(Ca2+)信号功能失调相关的人类疾病遗传基础的鉴定,引发了人们对调节细胞内Ca2+稳态的分子成分功能特性的极大兴趣。人们越来越认识到细胞内对ryanodine敏感的Ca2+释放通道(RyR)调节在骨骼肌和心肌病理状态(包括恶性高热、心力衰竭和心源性猝死)中的核心作用。克隆的RyR亚型和重组表达技术的应用极大地促进了对RyR Ca2+释放功能分子基础的阐明。本综述将聚焦于用于重组RyR亚型功能特性鉴定的重组技术,以及这些方法在揭示RyR通道功能机制基础方面所获得的见解。