致心律失常性右室发育不良表现为右室流出道心动过速。

Arrhythmogenic right ventricular dysplasia presenting as right ventricular outflow tract tachycardia.

作者信息

Sticherling Christian, Zabel Markus

机构信息

Division of Cardiology, University Hospital Basel, Petersgraben 4, 4031 Basel, Switzerland.

出版信息

Europace. 2005 Jul;7(4):345-7. doi: 10.1016/j.eupc.2005.03.004.

DOI:10.1016/j.eupc.2005.03.004

PMID:15944092

Abstract

A case of a 51-year old male is presented. A left bundle branch block inferior axis tachycardia was manifest. At electrophysiological study this tachycardia was inducible and was ablated in the septal right ventricular outflow tract (RVOT). Two other tachycardias were identified both with right bundle branch block (RBBB) morphology raising the suspicion of diffuse pathology. Arrythmogenic right ventricular dysplasia (ARVD) was confirmed by right ventricular angiography and magnetic resonance imaging (MRI). An implantable cardioverter defibrillator (ICD) was implanted and an appropriate shock was later delivered.

摘要

报告一例51岁男性病例。该患者表现为左束支传导阻滞伴下轴心动过速。在电生理研究中，这种心动过速可诱发，并在右心室流出道间隔部成功消融。另外还发现了另外两种心动过速，均具有右束支传导阻滞（RBBB）形态，这增加了弥漫性病变的怀疑。右心室造影和磁共振成像（MRI）证实为致心律失常性右心室发育不良（ARVD）。植入了植入式心脏复律除颤器（ICD），随后进行了一次恰当的电击。