新生儿黑色素性神经外胚层肿瘤

Melanotic neuroectodermal tumor in a newborn.

作者信息

Tan Onder, Atik Bekir, Ugras Serdar

机构信息

Ataturk University, Medical Faculty, Department of Plastic Reconstructive and Aesthetic Surgery, 25240 Erzurum, Turkey.

出版信息

Int J Pediatr Otorhinolaryngol. 2005 Oct;69(10):1441-4. doi: 10.1016/j.ijporl.2005.04.024.

DOI:10.1016/j.ijporl.2005.04.024

PMID:15963575

Abstract

Melanotic neuroectodermal tumor of infancy (MNTI) is an uncommon, fast-growing, pigmented neoplasm of neural crest origin; it primarily affects the maxilla of the infants during the first year of life. Approximately 200 instances of this tumor are reported in the medical literature. We present a case of newborn with MNTI on the left maxillary alveolar ridge. The patient underwent complete surgical resection without maxillectomy. There has been no recurrence in a follow-up period of 1 year. The diagnostic features and management alternatives of MNTI are discussed.

摘要

婴儿黑色素性神经外胚层肿瘤（MNTI）是一种罕见的、生长迅速的、起源于神经嵴的色素性肿瘤；它主要在婴儿出生后的第一年影响上颌骨。医学文献中报道了约200例这种肿瘤。我们报告一例左侧上颌牙槽嵴患有MNTI的新生儿病例。该患者接受了完整的手术切除，未进行上颌骨切除术。在1年的随访期内未出现复发。本文讨论了MNTI的诊断特征和治疗选择。