Cauchi John A, Chandran Harish
Department of Paediatric Surgery, Birmingham Children's Hospital, Steelhouse Lane, Birmingham, B4 6NH, UK.
Pediatr Surg Int. 2005 Jul;21(7):566-8. doi: 10.1007/s00383-005-1455-0. Epub 2005 Jun 17.
Often misdiagnosed as primary megaureter or pelviureteric junction obstruction, congenital ureteral stenosis and valves are the main causes of congenital ureteric obstruction. We report three consecutive cases of congenital ureteric strictures presenting with antenatally diagnosed hydronephrosis. Two of our cases had a contralateral multicystic dysplastic kidney. We discuss the aetiology, clinical presentation, diagnostic evaluation, surgical management, and operative results as well as present an overview of the international literature, highlighting the importance of early referral in cases of contralateral abnormality as well as the importance of performing a retrograde study to facilitate the diagnosis and choice of incision.
先天性输尿管狭窄和瓣膜常被误诊为原发性巨输尿管或肾盂输尿管连接处梗阻,是先天性输尿管梗阻的主要原因。我们报告了连续3例先天性输尿管狭窄病例,均在产前诊断为肾积水。其中2例对侧有多囊肾发育不良。我们讨论了病因、临床表现、诊断评估、手术治疗及手术结果,并对国际文献进行了综述,强调了对侧异常情况下早期转诊的重要性,以及进行逆行检查以辅助诊断和选择切口的重要性。