Chen Wei-Jen, Chen Wei-Ming, Chiang Chao-Ching, Huang Ching-Kuei, Chen Tain-Hsiung, Lo Wai-Hee
Department of Orthopedics and Traumatology, Taipei Veterans General Hospital, Taipei, Taiwan, R.O.C.
J Chin Med Assoc. 2005 Jul;68(7):343-6. doi: 10.1016/S1726-4901(09)70173-X.
Fibrous dysplasia, a condition in which the skeleton fails to develop normally, is characterized by fibroblastic stroma and immature bone. Bowing of the long bones occurs frequently in the polyostotic form, and stress fractures often result. Shepherd's crook deformity is a characteristic feature of fibrous dysplasia. The goal of its treatment is to obtain normal walking ability and relieve pain due to pathologic fracture secondary to the deformity; however, correction of the deformity is a surgical challenge. We present 2 cases of shepherd's crook deformity treated with corrective osteotomy and a dynamic hip screw. Both cases showed good bone healing and no recurrent deformity. The gross deformities were corrected, and both patients were pain-free after operation.
纤维性发育不良是一种骨骼无法正常发育的病症，其特征为成纤维细胞基质和未成熟骨。长骨弯曲在多骨型纤维性发育不良中经常出现，且常导致应力性骨折。牧羊人手杖样畸形是纤维性发育不良的一个特征性表现。其治疗目标是获得正常行走能力并缓解因畸形继发的病理性骨折所致的疼痛；然而，畸形矫正仍是一项外科挑战。我们报告2例采用截骨矫形术和动力髋螺钉治疗的牧羊人手杖样畸形病例。两例均显示良好的骨愈合且无畸形复发。严重畸形得到矫正，两名患者术后均无疼痛。
