Simon Scott L, Moonis Gul, Judkins Alexander R, Scobie Janice, Burnett Mark G, Riina Howard A, Judy Kevin D
Department of Neurosurgery, The Hospital of the University of Pennsylvania, Philadelphia, PA 19104, USA.
Surg Neurol. 2005 Aug;64(2):154-9. doi: 10.1016/j.surneu.2004.10.025.
Capillary hemangiomas are benign vascular lesions that commonly present at birth or in early infancy on the face, scalp, back, or chest. The authors present an exceedingly rare case of an intracranial capillary hemangioma arising in an adult. Only 4 biopsy-proven cases have been reported in the pediatric population previous to this case report.
A 31-year-old pregnant woman presented at 38 weeks of gestation with severe headaches, nausea, and vomiting. Imaging revealed an extra-axial mass lesion arising from the tentorium with both supra- and infratentorial components. The patient underwent a resection of her tumor, which was diagnosed as a capillary hemangioma by histopathologic examination. The patient required 2 further resections after the lesion exhibited a rapid regrowth from residual tumor in the left transverse sinus. The patient has remained free of disease 41 months out from her third surgery.
Intracranial capillary hemangiomas are exceedingly rare entities, with a capability for rapid growth. When gross total resection cannot be achieved, these patients should be observed closely, and the use of adjuvant radiotherapy should be considered.
毛细血管瘤是一种良性血管病变,通常在出生时或婴儿早期出现在面部、头皮、背部或胸部。作者报告了一例极为罕见的发生于成人的颅内毛细血管瘤病例。在此病例报告之前,儿科人群中仅有4例经活检证实的病例报道。
一名31岁的孕妇在妊娠38周时出现严重头痛、恶心和呕吐。影像学检查显示,一个起源于小脑幕的轴外肿块病变,同时累及幕上和幕下部分。患者接受了肿瘤切除术,经组织病理学检查诊断为毛细血管瘤。在病变从左横窦的残留肿瘤迅速复发后,患者又接受了两次手术切除。患者在第三次手术后41个月一直无病生存。
颅内毛细血管瘤极为罕见,具有快速生长的能力。当无法实现全切时,应密切观察这些患者,并考虑使用辅助放疗。