Harris K M, Lloyd D C, Morrissey B, Adams H
Department of Radiology, Llandough Hospital, Penarth, South Glamorgan.
Clin Radiol. 1992 Jun;45(6):382-6. doi: 10.1016/s0009-9260(05)80995-x.
Isolated pulmonary artery atresia is an uncommon congenital abnormality. Plain radiography and ventilation/perfusion lung scintigraphy may suggest the diagnosis but pulmonary angiography has traditionally been recommended for confirmation. The computed tomographic (CT) appearances of four patients with isolated atresia of a pulmonary artery are described. In each case the atretic segment of the abnormal vessel could be identified. Other CT findings included reduction of volume of the involved hemithorax, increased density of the affected lung, a small hilum, and an abnormal pulmonary vascular pattern thought to be due to the collateral systemic arterial supply to the intrapulmonary branches of the atretic pulmonary artery. The diagnosis of isolated pulmonary artery atresia can be made using dynamic, contrast enhanced CT without recourse to more invasive procedures.
孤立性肺动脉闭锁是一种罕见的先天性异常。胸部X线平片和通气/灌注肺闪烁扫描可能提示诊断，但传统上推荐进行肺动脉造影以确诊。本文描述了4例孤立性肺动脉闭锁患者的计算机断层扫描（CT）表现。在每例病例中，均可识别出异常血管的闭锁段。其他CT表现包括患侧半胸容积减小、患肺密度增加、肺门变小以及异常的肺血管形态，认为这是由于闭锁肺动脉的肺内分支存在体循环动脉侧支供血所致。使用动态对比增强CT即可诊断孤立性肺动脉闭锁，无需采用更具侵入性的检查方法。
