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纵隔黏液乳头型室管膜瘤或尾骨旁室管膜瘤的原发性或晚期转移:1例报告

Mediastinal myxopapillary ependymoma primary or late metastases of paracoccygeal ependymoma: a case report.

作者信息

Satti Mohammed, Firoze Mohamed, Malaker Kamal, Hussain Mohammed, Maniyar Iqbal

机构信息

Department of Pathology, King Abdulaziz Medical City, National Guard Health Affairs, Jeddah 21423, KSA.

出版信息

Ann Diagn Pathol. 2005 Aug;9(4):215-8. doi: 10.1016/j.anndiagpath.2005.04.015.

DOI:10.1016/j.anndiagpath.2005.04.015
PMID:16084455
Abstract

A 25-year-old woman presented in 2002 with progressive shortness of breath and weight loss. A computed tomographic scan of the chest showed a huge anterior mediastinal mass, and pathological examination of a mediastinoscopic needle biopsy revealed typical myxopapillary ependymoma, an extremely unusual diagnosis at this site. Further workup and questioning of the patient revealed that she had opted not to disclose a history of surgery for right gluteal fold mass in 1993, which was primarily treated with surgery followed by radiotherapy for relapse. Review of the histology of the excised mass showed a myxopapillary ependymoma, similar to current histology. Clinical examination of the local gluteal and paracoccygeal site, computed tomographic imaging, and magnetic resonance imaging failed to demonstrate any evidence of recurrent disease in soft tissue or bone. The case is presented, and this very unusual presentation is discussed.

摘要

一名25岁女性于2002年出现进行性气短和体重减轻。胸部计算机断层扫描显示前纵隔有巨大肿块,纵隔镜针吸活检的病理检查显示为典型的黏液乳头型室管膜瘤,这在此部位是极其罕见的诊断。对患者进一步检查和询问发现,她未提及1993年有过右臀褶肿块手术史,该肿块最初接受手术治疗,复发后进行了放疗。对切除肿块的组织学复查显示为黏液乳头型室管膜瘤,与当前组织学表现相似。对局部臀肌和尾骨旁部位的临床检查、计算机断层成像及磁共振成像均未发现软组织或骨骼有复发病灶的任何证据。现报告该病例,并讨论这种非常不寻常的表现。

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