Dearani Joseph A, Danielson Gordon K
Division of Cardiovascular Surgery, Mayo Clinic College of Medicine, Rochester, Minnesota 55902, USA.
Semin Thorac Cardiovasc Surg. 2005 Summer;17(2):148-54. doi: 10.1053/j.semtcvs.2005.02.008.
Ebstein's anomaly is a rare cardiac malformation that affects the tricuspid valve, right ventricle, and right atrioventricular junction. These anatomical and functional abnormalities cause important tricuspid regurgitation that results in right atrial and right ventricular dilatation and atrial and ventricular arrhythmias. Diagnosis is made by echocardiography. Operation includes tricuspid valve repair or replacement, closure of any interatrial communications, and appropriate antiarrhythmia procedures. Repair of Ebstein's anomaly eliminates right-to-left intracardiac shunting, improves exercise tolerance and functional class, and reduces supraventricular arrhythmias. In addition, quality of life and longevity are improved.
埃布斯坦畸形是一种罕见的心脏畸形，累及三尖瓣、右心室和右房室交界处。这些解剖和功能异常导致严重的三尖瓣反流，进而引起右心房和右心室扩张以及房性和室性心律失常。通过超声心动图进行诊断。手术包括三尖瓣修复或置换、关闭任何心房内交通以及适当的抗心律失常程序。埃布斯坦畸形的修复消除了心内右向左分流，提高了运动耐量和心功能分级，并减少了室上性心律失常。此外，生活质量和寿命也得到了改善。
