Hanna Dominique, Cloutier Richard, Lapointe Roch, Desgagné Antoine
Dermatology department, CHUQ Hotel-Dieu de Québec, 11 cote du Palais, G1R 2J6, Ste-Foy, Québec, Canada.
J Cutan Med Surg. 2004 Jul-Aug;8(4):229-32. doi: 10.1007/s10227-003-0104-2.
Elephantiasis is a well-known condition in dermatology usually affecting the legs and external genitalia. It is characterized by chronic inflammation and obstruction of the lymphatic channels and by hypertrophy of the skin and subcutaneous tissues. The etiology is either idiopathic or caused by a variety of conditions such as chronic filarial disease, leprosy, leishmaniasis, and chronic recurrent cellulites.
Elephantiasis of the abdominal wall is very rare. A complete review of the English and French literature showed only two cases reported in 1966 and 1973, respectively. We report a third case of abdominal elephantiasis and we briefly review this entity.
We present the case of a 51-year-old woman who had progressively developed an enormous pediculated abdominal mass hanging down her knees. The skin was thickened, hyperpigmented, and fissured. She had a history of multiple abdominal cellulites.
She underwent an abdominal lipectomy. Histopathology of the specimen confirmed the diagnosis of abdominal elephantiasis.
Abdominal elephantiasis is a rare disease that represents end-stage failure of lymph drainage. Lipectomy should be considered in the management of this condition.
象皮肿是皮肤病学中一种众所周知的病症,通常影响腿部和外生殖器。其特征为淋巴管的慢性炎症和阻塞以及皮肤和皮下组织的肥大。病因要么是特发性的,要么由多种病症引起,如慢性丝虫病、麻风病、利什曼病和慢性复发性蜂窝织炎。
腹壁象皮肿非常罕见。对英文和法文文献的全面检索显示,分别在1966年和1973年仅有两例报告。我们报告第三例腹壁象皮肿病例并简要回顾这一病症。
我们介绍一名51岁女性的病例,她逐渐出现一个巨大的带蒂腹部肿物,垂至膝部。皮肤增厚、色素沉着且有裂隙。她有多次腹部蜂窝织炎病史。
她接受了腹部脂肪切除术。标本的组织病理学证实了腹壁象皮肿的诊断。
腹壁象皮肿是一种罕见疾病,代表淋巴引流的终末期衰竭。在这种病症的治疗中应考虑脂肪切除术。