Roupret Morgan, Beley Sébastien, Traxer Olivier, Kirsch-Noir Frédérique, Jouannet Pierre, Jardin Alain, Thiounn Nicolas
Service d'Urologie, Hôpital Tenon, Paris, France.
Prog Urol. 2005 Jun;15(3):392-6; discussion 396-7.
Sickle-cell anaemia is an autosomal recessive hereditary haemoglobinopathy. Patients with sickle-cell anaemia present a high risk of priapism. At least 40% of sickle-cell patients report episodes of priapism. Priapism in patients with sickle-cell tend to start during childhood and rapidly threaten the erectile prognosis. Apart from specific treatment of sickle-cell anaemia, the urologist must be able to recognize forms of intermittent priapism and promote medical prevention. The urologist must also be able to distinguish low-flow priapism from the rarer high-flow priapism, as the treatments differ. Treatment strategies are increasingly well defined, with an increasingly limited place for surgery.
镰状细胞贫血是一种常染色体隐性遗传性血红蛋白病。镰状细胞贫血患者发生阴茎异常勃起的风险很高。至少40%的镰状细胞病患者报告有阴茎异常勃起发作。镰状细胞病患者的阴茎异常勃起往往始于儿童期,并迅速威胁勃起预后。除了镰状细胞贫血的特异性治疗外,泌尿科医生必须能够识别间歇性阴茎异常勃起的形式并促进医学预防。泌尿科医生还必须能够区分低流量阴茎异常勃起和较罕见的高流量阴茎异常勃起,因为治疗方法不同。治疗策略越来越明确,手术的应用越来越有限。