Dovlatian A A
Urologiia. 2005 May-Jun(3):38-43.
Ten clinical cases of neuromuscular dysplasia of the ureter (NMDU) are reported. Eight patients were young (24-38 years), two--of the middle age (41-58 years). NMDU was bilateral in two patients. Ureteral achalasia of the congenital solitary kidney occured in one case. One 28-year-old female with megaureter of the solitary kidney had interstitial cystitis. Clinical picture of the disease was characterized primarily with acute pyelonephritis, pain and secondary urolithiasis. Surgical treatment consisted in resection of the affected part of the ureter with modeling of the lumen of the latter on the drainage and Boari plastic repair. Bilateral Boari operation was made in 2 patients. In one case of ureteral achalasia and ureterocele direct ureterocystoanastomosis was created with good result. Sigmocystoplasty with transplantation of the solitary kidney ureter into the intestinal transplant was made in the patient with scar contracture of the detrusor and megaureter. Functional result of the operation was good. Complications were registered in 4 patients, 2 of which were reoperated. In nine patients of ten good and satisfactory functional results were obtained.
报告了10例输尿管神经肌肉发育异常（NMDU）的临床病例。8例患者为年轻人（24 - 38岁），2例为中年人（41 - 58岁）。2例患者为双侧NMDU。1例先天性孤立肾出现输尿管失弛缓症。1例28岁孤立肾巨输尿管女性患有间质性膀胱炎。该疾病的临床表现主要为急性肾盂肾炎、疼痛和继发性尿路结石。手术治疗包括切除输尿管的受累部分，并根据引流情况对输尿管管腔进行塑形以及Boari整形修复。2例患者进行了双侧Boari手术。1例输尿管失弛缓症和输尿管囊肿患者进行了直接输尿管膀胱吻合术，效果良好。对1例逼尿肌瘢痕挛缩和巨输尿管患者进行了乙状结肠膀胱成形术，并将孤立肾输尿管移植到肠道移植物中。手术功能结果良好。4例患者出现并发症，其中2例再次手术。10例患者中有9例获得了良好和满意的功能结果。
