Sakai T, Vallejo M C, Shannon K T
Department of Anesthesiology, Magee Women's Hospital, University of Pittsburgh School of Medicine, Pittsburgh, PA 15213, USA.
Int J Obstet Anesth. 2005 Oct;14(4):332-5. doi: 10.1016/j.ijoa.2005.02.007.
Neurofibromatosis type 2 is an extremely rare form of neurofibromatosis characterized by central nervous system involvement with bilateral vestibular schwannomas and spinal tumors. Anesthetic management of a parturient with neurofibromatosis type 2 has not been fully reported, and the condition is challenging to obstetric anesthesiologists due to the presence of intracranial and intraspinal canal neurofibromas. We present a case of neurofibromatosis type 2 referred for delivery. Because of central neuraxial involvement, regional anesthesia was avoided, and the patient delivered by cesarean section under general anesthesia. The importance of pre-operative diagnosis and multidisciplinary management for neurofibromatosis type 2 is emphasized and anesthetic and obstetric considerations for delivery are presented.
2型神经纤维瘤病是一种极为罕见的神经纤维瘤病,其特征是中枢神经系统受累,伴有双侧前庭神经鞘瘤和脊柱肿瘤。2型神经纤维瘤病产妇的麻醉管理尚未得到充分报道,由于存在颅内和椎管内神经纤维瘤,这种情况对产科麻醉医生来说具有挑战性。我们报告一例因分娩转诊的2型神经纤维瘤病病例。由于中枢神经轴受累,避免了区域麻醉,患者在全身麻醉下剖宫产分娩。强调了2型神经纤维瘤病术前诊断和多学科管理的重要性,并介绍了分娩时的麻醉和产科注意事项。