Marandian M H, Foroozanfar N, Haghigat H, Saket S, Lessani M, Djafarian M
Arch Fr Pediatr. 1979 Sep-Oct;36(8):819-22.
Seven cases of Papillon-Lefevre syndrome are described, 4 children and their mother with two other relatives on the mother's side. An immune defect was suspected because six of the seven had a history of severe pyogenic infections, but the results of the tests were not the same in the three individuals tested. In one patient no immune defect was detected but in the other two the response of lymphocytes to candida and to streptokinase and streptodornase was reduced.
本文描述了7例帕皮永-勒费夫尔综合征患者，其中包括4名儿童及其母亲，以及母亲一方的另外两名亲属。由于7例患者中有6例有严重化脓性感染病史，因此怀疑存在免疫缺陷，但在接受检测的3人中，检测结果并不相同。1例患者未检测到免疫缺陷，而另外2例患者淋巴细胞对念珠菌、链激酶和链道酶的反应减弱。
