Ince Erdal, Ciftçi Ergin, Tekin Mustafa, Kendirli Tanil, Tutar Ercan, Dalgiç Nazan, Oncel Selim, Dogru Ulker
Division of Pediatric Infectious Disease, Department of Pediatrics, Ankara Univeristy School of Medicine, Dikimevi, Ankara, Turkey.
Pediatr Int. 2005 Oct;47(5):550-3. doi: 10.1111/j.1442-200x.2005.02124.x.
Thermoregulation problems, resulting in hypo- or hyperthermia, have been infrequently reported in children with Prader Willi syndrome (PWS), yet their clinical details remained unknown.
The clinical characteristics of three infants with PWS are reported.
Etiologies of high fever could not be identified in three children with PWS. One of these children was also admitted to the intensive care unit with extremely high body temperature in a life-threatening condition, similar to septic shock, without a plausible explanation.
Hyperthermia may be a part of the clinical spectrum in young infants with PWS and should be carefully monitored, since it may cause life-threatening complications.
体温调节问题导致体温过低或过高，在普拉德-威利综合征（PWS）患儿中鲜有报道，但其临床细节仍不为人知。
报告了3例PWS婴儿的临床特征。
3例PWS患儿的高热病因均无法明确。其中1例患儿还因体温极高被送入重症监护病房，处于类似感染性休克的危及生命状态，且无合理的解释。
体温过高可能是PWS幼儿临床症状的一部分，应予以密切监测，因为它可能导致危及生命的并发症。
