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妊娠合并植入式心律转复除颤器的致心律失常性右室心肌病

Arrhythmogenic right ventricular cardiomyopathy with implantable cardioverter defibrillator placement in pregnancy.

作者信息

Doyle Nora M, Monga Manju, Montgomery Baxter, Dougherty Anne H

机构信息

Division of Maternal Fetal Medicine, Department of Obstetrics, Gynecology, and Reproductive Sciences, University of Texas Houston Medical School, Houston, Texas 77030, USA.

出版信息

J Matern Fetal Neonatal Med. 2005 Aug;18(2):141-4. doi: 10.1080/14767050500226500.

DOI:10.1080/14767050500226500
PMID:16203602
Abstract

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a disorder that predominantly affects the right side of the heart and causes ventricular arrhythmias. In many patients the disease is familial. ARVC may account for as many as 5% of unexpected sudden deaths. We report a case of ARVC diagnosed at 21 weeks gestation treated with an implantable cardiac defibrillator. The remainder of her pregnancy was uneventful and the patient underwent induction of labor at 39 weeks gestation with a passive second stage forceps-assisted delivery resulting in delivery of a normal infant. In the gravida with cardiac arrhythmias, defibrillator placement may offer a safe, life-preserving treatment and should be considered.

摘要

致心律失常性右室心肌病(ARVC)是一种主要累及心脏右侧并导致室性心律失常的疾病。在许多患者中,该疾病具有家族性。ARVC可能占意外猝死病例的5%。我们报告一例在妊娠21周时诊断为ARVC并接受植入式心脏除颤器治疗的病例。她妊娠的其余过程顺利,患者在妊娠39周时引产,第二产程采用被动产钳助产,分娩出一名正常婴儿。对于患有心律失常的孕妇,植入除颤器可能是一种安全的、挽救生命的治疗方法,应予以考虑。

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