Pereira Regina Maria, Simões e Silva Ana Cristina, Leite Virgínia Hora Rios, Lanna José Carlos Brandão Duarte, Guimarães José Teixeira
Department of Pediatrics, School of Medicine, Federal University of Minas Gerais (UFMG), Belo Horizonte, Gerais 30140-061, Brazil.
J Pediatr Surg. 2005 Oct;40(10):e21-4. doi: 10.1016/j.jpedsurg.2005.06.034.
We report the second case in literature of a boy with the association of large omphalocele, accessory hepatic lobe, and biliary atresia, and the first successful treatment. The patient was submitted to a surgical treatment at 44 days of life, including Kasai procedure, correction of the remnant abdominal wall defect, and removal of a hepatic accessory lobe. The boy evolved with normalization of hepatic function tests. After 15 years of follow-up, the patient is completely healthy, weights 45 kg, and is 1.64 m tall.
我们报告了文献中第二例患有巨大脐膨出、副肝叶和胆道闭锁的男孩病例，也是首例成功治疗的病例。该患者在出生44天时接受了手术治疗，包括Kasai手术、残余腹壁缺损修复以及副肝叶切除。术后男孩肝功能检查恢复正常。经过15年的随访，患者完全健康，体重45公斤，身高1.64米。
