Scherak O Smolen J S, Smolen J S, Menzel E J, Kolarz G
Acta Med Austriaca. 1979;6(5):214-6.
A case report of a patient with essential cryoglobulinemia and episodes of angioedema caused by an acquired C1 inhibitor deficiency is presented. The patient had high levels of circulating immune complexes. In the course of complement activation C1 inhibitor may be consumed and the resulting C1 inhibitor deficiency led to the occurrence of angioedema.
本文报告一例原发性冷球蛋白血症患者,其血管性水肿发作由获得性C1抑制物缺乏引起。患者循环免疫复合物水平较高。在补体激活过程中,C1抑制物可能被消耗,由此产生的C1抑制物缺乏导致血管性水肿的发生。