Trasi Sucheta, Mohanty Dipika, Shetty Shrimati, Ghosh Kanjaksha
Institute of Immunohaematology (ICMR), KEM Hospital campus, Parel, Mumbai, Maharashtra, India.
Natl Med J India. 2005 Jul-Aug;18(4):187-8.
We report the successful prenatal diagnosis of von Willebrand disease (VWD) in a family with type 3 severe VWD by the indirect method of gene tracking using polymorphic markers of intron 40 of the von Willebrand factor (VWF) gene. The couple had a daughter diagnosed to have type 3 VWD. Chorionic villus sampling (CVS) was done in the eleventh week of gestation of a subsequent pregnancy. The 3 VNTR polymorphic markers VWF1, VWF2 and VWF3 of intron 40 of the VWF gene were used for linkage studies. DNA in the affected VWD patient, the father and mother as well as in the CVS using VWF1 and VWF3 polymorphic markers revealed that the foetus was affected. The family chose to abort the foetus. In a subsequent pregnancy, similar investigation revealed a normal foetus. Prenatal diagnosis in families with a diagnosed case of VWD can be used to determine the status of the foetus. The technique is inexpensive.
我们报告了通过使用血管性血友病因子(VWF)基因第40内含子的多态性标记进行基因追踪的间接方法,成功对一个患有3型严重血管性血友病(VWD)的家庭进行了产前诊断。这对夫妇有一个被诊断为3型VWD的女儿。在随后一次妊娠的第11周进行了绒毛取样(CVS)。使用VWF基因第40内含子的3个VNTR多态性标记VWF1、VWF2和VWF3进行连锁研究。对受影响的VWD患者、父亲和母亲以及使用VWF1和VWF3多态性标记的CVS中的DNA进行检测,结果显示胎儿受到影响。该家庭选择终止妊娠。在随后的一次妊娠中,类似的检查显示胎儿正常。对于已诊断出VWD病例的家庭,产前诊断可用于确定胎儿的状况。该技术成本低廉。