Dileo Palma, Demetri George D
Dana-Farber Cancer Institute, Harvard Medical School, Boston, MA 02115, USA.
Clin Adv Hematol Oncol. 2005 Oct;3(10):781-91.
Sarcomas represent a family of uncommon malignancies related by histopathology and developmental biology. Sarcomas arise from any of the mesodermal tissues anywhere in the body (muscles, tendons, adipose tissue, blood vessels, and joints) from cells of mesenchymal origin or in the peripheral nervous system, derived from the ectoderm. Mainly diagnosed in the extremities, sarcomas can be present also in soft tissues of the trunk, abdomen, and retroperitoneum, as well as the head and neck. During the last decade, improvements in diagnostic techniques have made it possible to identify and characterize a subset of sarcomas arising within the gastrointestinal tract known as gastrointestinal stromal tumors, which were previously commonly misclassified as leiomyosarcomas. Sarcomas are extremely heterogeneous, so expert histopathologic characterization is essential to choose the appropriate path of multidisciplinary treatment and predict possible clinical outcomes. The aim of this review is to provide a brief overview of the epidemiology, pathology, clinical presentation, and new approaches to the treatment of adult soft-tissue and bone sarcomas.
肉瘤是一类由组织病理学和发育生物学相关联的罕见恶性肿瘤。肉瘤起源于身体任何部位的中胚层组织(肌肉、肌腱、脂肪组织、血管和关节)的间充质来源细胞,或起源于外胚层衍生的周围神经系统。肉瘤主要诊断于四肢,也可出现在躯干、腹部和腹膜后的软组织,以及头颈部。在过去十年中,诊断技术的进步使得识别和表征胃肠道内出现的一类肉瘤——胃肠道间质瘤成为可能,这类肿瘤以前通常被错误地归类为平滑肌肉瘤。肉瘤具有极高的异质性,因此专业的组织病理学特征对于选择合适的多学科治疗路径和预测可能的临床结果至关重要。本综述的目的是简要概述成人软组织和骨肉瘤的流行病学、病理学、临床表现及新的治疗方法。