Gosalbez Rafael, Castellan Miguel, Ibrahim Emad, DiSandro Michael, Labbie Andrew
Division of Pediatric Urology, Miami Children's Hospital and Jackson Memorial Hospital, University of Miami, Miami, FL, USA.
J Urol. 2005 Dec;174(6):2350-3, discussion 2353. doi: 10.1097/01.ju.0000180419.62193.78.
We retrospectively evaluated the results of an original technique that combines mobilization of the urogenital sinus with the creation of urogenital flaps to enlarge the vaginal introitus for 1-stage feminizing genitoplasty in children with urogenital sinus anomalies, thus, avoiding the use of posteriorly based perineal flaps.
A total of 11 patients with urogenital sinus anomalies have undergone a modified Fortunoff technique combining total urogenital mobilization with the creation of urogenital sinus flaps by a single surgeon (RG) since 1998. Patient age at surgery ranged from 3 months to 13 years (mean 3.8 years). Diagnoses included congenital adrenal hyperplasia in 7 patients, cloacal malformation in 2 and urogenital sinus malformation in 2. Eight patients underwent a perineal approach and 3 underwent a posterior sagittal approach.
Followup ranged from 3 months to 5 years (mean 2.5 years). The cosmetic appearance was considered superior to that achieved with previous techniques. The vagina had a more physiological position in all patients except 1, and no patient had development of vaginal stenosis. One patient had development of a mild mid urethral stricture that required a single dilation using anesthesia. In this patient cystourethroscopy performed 3 years later was normal.
We believe that the redundant urogenital sinus tissue must not be discarded, but rather incorporated into the reconstruction of the posterior vaginal wall, thus, avoiding the use of perineal skin flaps. This modification allows placement of the vaginal opening in a more physiological position with a better cosmetic appearance than previous techniques.
我们回顾性评估了一种原创技术的结果,该技术将泌尿生殖窦的游离与泌尿生殖皮瓣的创建相结合,以扩大泌尿生殖窦异常患儿一期女性化生殖器成形术的阴道入口,从而避免使用基于会阴后部的皮瓣。
自1998年以来,共有11例泌尿生殖窦异常患者接受了改良的福尔图诺夫技术,该技术由单一外科医生(RG)将泌尿生殖系统完全游离与创建泌尿生殖窦皮瓣相结合。手术时患者年龄从3个月至13岁(平均3.8岁)。诊断包括7例先天性肾上腺增生、2例泄殖腔畸形和2例泌尿生殖窦畸形。8例患者采用会阴入路,3例采用后矢状入路。
随访时间为3个月至5年(平均2.5年)。外观被认为优于以前的技术。除1例患者外,所有患者的阴道位置更符合生理状态,且无患者出现阴道狭窄。1例患者出现轻度尿道中段狭窄,需要在麻醉下进行单次扩张。该患者3年后进行的膀胱尿道镜检查结果正常。
我们认为,多余的泌尿生殖窦组织不应丢弃,而应纳入阴道后壁重建,从而避免使用会阴皮瓣。这种改良使得阴道口位置更符合生理状态,外观比以前的技术更好。