Okafuji Takashi, Yabuuchi Hidetake, Soeda Hiroyasu, Takahashi Naoki, Hatakenaka Masamitsu, Sakai Shuji, Nishihara Yunosuke, Noda Naotaka, Inoshima Ichiro, Honda Hiroshi
Department of Clinical Radiology, Graduate School of Medical Sciences, Kyushu University, Higashi-ku, Fukuoka, Japan.
J Thorac Imaging. 2005 Nov;20(4):284-7. doi: 10.1097/01.rti.0000186997.38447.47.
We report a case of Gorham's disease of the chest wall in a 29-year-old man. A chest radiograph showed osteolysis of the left first, second, and third ribs. CT and MR images revealed a soft tissue mass around the affected ribs. The mass presented as having heterogeneous high signal intensity on T2-weighted MR images, and it showed minimal enhancement on contrast-enhanced MR images. A histologic specimen obtained by incisional biopsy from the left third rib revealed proliferation of lymphangiomatous tissue in the bone marrow. A diagnosis of Gorham's disease was made based on these clinical, radiologic, and histologic findings.
我们报告一例29岁男性胸壁戈谢病。胸部X线片显示左侧第一、二、三根肋骨骨质溶解。CT和MR图像显示患侧肋骨周围有一软组织肿块。该肿块在T2加权MR图像上呈不均匀高信号强度，在对比增强MR图像上强化不明显。通过对左侧第三肋骨进行切开活检获得的组织学标本显示骨髓中淋巴管瘤组织增生。根据这些临床、放射学和组织学表现作出了戈谢病的诊断。
