Nayak U A, Rao A P, Sugumaran D K, Meenakshi Sundaram A L
Department of Pedodontics and Preventive Dentistry, Rajah Muthiah Dental College and Hospital, Annamalai University.
Indian J Dent Res. 2005 Jan-Mar;16(1):27-31.
Lobster-Claw syndrome is a rare autosomal dominant, hand-foot malformation with Oro-dental features. This is a rare condition and from the available reports so far, cases being reported are less than 1%. Most reports have focused on the hand-foot deformity of this syndrome. This paper highlights the typical Oro-dental features associated with this syndrome such as retained deciduous teeth, hypodontia and variation in crown size, arch length and arch width.
龙虾爪综合征是一种罕见的常染色体显性遗传病，伴有口面部特征的手足畸形。这是一种罕见病症，从目前可得的报告来看，所报告的病例不到1%。大多数报告都聚焦于该综合征的手足畸形。本文着重介绍了与该综合征相关的典型口面部特征，如乳牙滞留、牙齿发育不全以及牙冠大小、牙弓长度和牙弓宽度的变异。
