Servelle M, Turiaf J, Albeaux-Fernet M, Laroche C, Bernier J J, Soulié J, Bacourt F, Chabot J, Fournier D, Andrieux J B
Sem Hop. 1975 Mar 8;51(12):799-806.
Fibrosis of the intestinal lymphatic vessels, produced in one case by tuberculosis and, in the other, by appendicitis and peritonitis, caused blockage of the main lymphatic vessels causing, clinically, a protein-losing enteropathy similar to that noted in congenital lymphatic diseases of childhood. In the laboratory, there was noted a fall in serum protein, lipid and cholesterol. A fat absorption test was very abnormal showing a flat curve. During laparotomy, there was discovered on the small intestine, the same layout of lymph vessels, resembling a lace network, as that observed in congenital malformations. Intestinal lymphography showed considerable stasis of the opaque substance and absence of injection of the lymph vessels in the mesentery.
一例因肺结核、另一例因阑尾炎和腹膜炎导致的肠淋巴管纤维化，致使主要淋巴管阻塞，临床上引发了一种类似于儿童先天性淋巴疾病中所见的蛋白丢失性肠病。在实验室检查中，发现血清蛋白、脂质和胆固醇水平下降。脂肪吸收试验结果非常异常，呈现出平坦曲线。剖腹手术时，在小肠上发现了与先天性畸形中观察到的相同的淋巴管布局，类似蕾丝网络。肠道淋巴造影显示造影剂大量淤滞，肠系膜淋巴管未显影。
