Guclu Ender, Tokmak Abdurrahman, Oghan Fatih, Ozturk Ozcan, Egeli Erol
Department of Otorhinolaryngology and Head and Neck Surgery, Duzce Faculty of Medicine, University of Abant Izzet Baysal, Duzce, Turkey.
Laryngoscope. 2006 Jan;116(1):151-3. doi: 10.1097/01.mlg.0000184511.86579.47.
The present case is a diffuse isolated plexiform neurofibroma of the tongue that was not associated with neurofibromatosis that we treated with intraoral surgery.
A case report.
We present a 5-year-old girl with isolated plexiform neurofibroma of the tongue with infiltration of the tongue base and review treatment approaches for this very rare tumor.
An intraoral approach appears to be a good alternative method that allows both an acceptable exposure for total excision and limited postoperative sequelae.
Isolated plexiform neurofibroma of the tongue is very rare. It causes a massive macroglossia that is progressive with advance of years and disturbs the patient's speech, occlusion, and tongue movements. Involvement of the tongue may be associated with infiltration into the deep structures of the neck by the tumor, thereby presenting considerable operative difficulties.
本病例为一例舌部弥漫性孤立性丛状神经纤维瘤,不伴有神经纤维瘤病,我们采用口腔内手术进行治疗。
病例报告。
我们报告一名5岁女童患有舌部孤立性丛状神经纤维瘤并累及舌根,同时回顾了针对这种极为罕见肿瘤的治疗方法。
口腔内入路似乎是一种很好的替代方法,既能实现完全切除所需的充分暴露,又能减少术后后遗症。
舌部孤立性丛状神经纤维瘤非常罕见。它会导致巨舌症,且随着年龄增长逐渐加重,影响患者的言语、咬合和舌运动。肿瘤累及舌部可能会浸润至颈部深部结构,从而带来相当大的手术困难。