Guan H
Zhonghua Yi Xue Za Zhi. 1991 Mar;71(3):144-6, 12.
Budd-Chiari syndrome is an unusual form of portal hypertension caused by liver cirrhosis. Its mortality rate exceeds 50% within 2 years. Surgical therapy provides superior survival rates than conservative medical management. During 1984-1989, 58 cases of Budd-Chiari syndrome were treated at PUMC hospital. The age of these patients ranged from 16 to 62. There were 39 males and 19 females. Diagnosis was mostly made by simultaneous inferior and superior Vena Cavography and one case was diagnosed by liver biopsy. Intraluminal pressure measurement of IVC and diameter measurement of IVC by Doppler ultrasound method were used for diagnosis. Preoperative intraluminal mean pressure of IVC in 26 cases was 3.2 +/- 0.6 kPa and it decreased to 1.9 +/- 0.6 kPa postoperatively. (P less than 0.01) Digital membranotomy through right atrium was done in 34 cases, percutaneous balloon catheter dilatation in 7 cases and Meso-atrial shunt, inferior Vena Cava Atrial shunt were performed in 20 cases. Postoperative improvement was found in 85% of the patients during the follow-up period (from 2-60 months).
布加综合征是由肝硬化引起的一种特殊类型的门静脉高压症。其2年内死亡率超过50%。手术治疗的生存率高于保守药物治疗。1984年至1989年期间，北京协和医院共治疗58例布加综合征患者。这些患者年龄在16岁至62岁之间。其中男性39例，女性19例。诊断主要通过同时进行下腔静脉造影和上腔静脉造影，1例通过肝活检确诊。采用多普勒超声方法测量下腔静脉腔内压力和下腔静脉直径进行诊断。26例患者术前下腔静脉腔内平均压力为3.2±0.6 kPa，术后降至1.9±0.6 kPa。（P<0.01）34例行经右心房数字膜切开术，7例行经皮球囊导管扩张术，20例行中房分流术、下腔静脉心房分流术。随访期间（2至60个月）85%的患者术后病情改善。
