[与腹部神经纤维肉瘤和嗜铬细胞瘤相关的I型神经纤维瘤病（冯·雷克林豪森病）。附病例报告]
[Type I neurofibromatosis (von Recklinghausen's disease) associated with abdominal neurofibrosarcoma and pheochromocytoma. Apropos of a case].
作者信息
De Grez T, Lambert M, Delaere B, Gigot J F, Haot J
机构信息
Service de Médecine Interne Générale, Cliniques Universitaires Saint-Luc, Bruxelles.
出版信息
Acta Clin Belg. 1991;46(2):89-93. doi: 10.1080/17843286.1991.11718148.
Abstract
Neoplasia and endocrine disorders are common complications of neurofibromatosis 1 (NF1--von Recklinghausen disease). We report here a case of NF1 in a 31-year-old woman presenting simultaneously with an abdominal neurofibrosarcoma and a pheochromocytoma. The prevalence of secondary neoplasia and endocrine tumors in NF1 is also discussed.
摘要
肿瘤形成和内分泌紊乱是1型神经纤维瘤病（NF1，即冯雷克林霍增氏病）的常见并发症。我们在此报告一例31岁女性的NF1病例，该患者同时患有腹部神经纤维肉瘤和嗜铬细胞瘤。本文还讨论了NF1中继发性肿瘤形成和内分泌肿瘤的患病率。
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