Piña Yigal, Exaire José E, Sandoval Julio
Instituto Nacional de Cardiología, Hemodinámica, Mexico City, Mexico.
J Invasive Cardiol. 2006 Mar;18(3):E102-4.
The compression of the left main coronary artery (LMCA) secondary to pulmonary artery trunk dilatation is a relatively new entity that has been associated with severe pulmonary hypertension. It is associated with acyanogen congenital cardiopathies or idiopathic pulmonary arterial hypertension. The natural history is unknown and its treatment has been based more on the severity of the angiographic compression than on the objective demonstration of myocardial ischemia. We report a case of a woman with severe pulmonary arterial hypertension due to an atrial septal defect with extrinsic compression of the LMCA and a physiopathologic approach to guide its treatment.
继发于肺动脉主干扩张的左冠状动脉主干（LMCA）受压是一种相对较新的疾病，与严重的肺动脉高压相关。它与非青紫型先天性心脏病或特发性肺动脉高压有关。其自然病史尚不清楚，其治疗更多地基于血管造影压迫的严重程度，而非心肌缺血的客观证据。我们报告一例因房间隔缺损导致严重肺动脉高压并伴有LMCA外在压迫的女性病例，以及一种指导其治疗的病理生理学方法。
