单羊膜囊双胎中的并腿畸形：一例病例报告。
Sirenomelia in a monoamniotic twin: a case report.
作者信息
Akl Mohamed N, Saleh Abdelaziz A
机构信息
Department of Obstetrics and Gynecology, Michigan State University, Hurley Medical Center, Flint, Michigan 48503, USA.
出版信息
J Reprod Med. 2006 Feb;51(2):138-40.
BACKGROUND
Sirenomelia is a rare congenital malformation characterized by fusion of the lower extremities and is associated with renal agenesis and absent bladder. Oligohydramnios usually occurs early in pregnancy.
CASE
A 21-year-old primigravida with a twin gestation was diagnosed with sirenomelia in 1 of the twins at 18 weeks; they were delivered at 34 weeks. The infant was in perfect respiratory condition, lived for 5 days and died of nonpulmonary causes.
CONCLUSION
Absence of oligohydramnios in monoamniotic twins allows free movement of the fetus in utero, facilitates the visualization of fetal organs on ultrasound and aids early prenatal diagnosis. It also delays the death of the sirenomelia infant due to the improved respiratory condition.
背景
美人鱼综合征是一种罕见的先天性畸形，其特征为下肢融合，并伴有肾缺如和膀胱缺如。羊水过少通常在妊娠早期出现。
病例
一名21岁的初产妇怀有双胎，在孕18周时诊断其中1个胎儿患有美人鱼综合征；孕34周时分娩。婴儿呼吸状况良好，存活5天，死于非肺部原因。
结论
单羊膜囊双胎中无羊水过少可使胎儿在子宫内自由活动，便于超声观察胎儿器官，有助于早期产前诊断。这也因呼吸状况改善而延迟了美人鱼综合征婴儿的死亡。
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