Simonovich Catherine J, Hardman John M, Navin James J, Jacobs Jennifer, Fergusson Neil
Department of Pathology, John A. Burns School of Medicine, Honolulu, HI 96813, USA.
Hawaii Med J. 2006 Jan;65(1):18-20.
We report the case of an 82-year-old woman who presented with an ill-defined mass and tenderness in the right lower quadrant of the abdomen. On computerized tomography scan, she had an irregular large bosselated mass of the mesentery located medial to the cecum and associated with multiple loops of small intestine. Preoperative differential diagnoses included leiomyosarcoma, lymphoma and gastrointestinal stromal tumor. The mesenteric mass was resected and identified as a leiomyosarcoma. This patient's tumor is typical of a mesenteric leiomyosarcoma and recurred with hepatic metastases two years after its initial removal. Such tumors usually do not become symptomatic until late in the course of disease, often after distant metastases have occurred. Mesenteric leiomyosarcomas are rare and have a reported incidence of 1: 350,000.
我们报告了一例82岁女性患者,其表现为右下腹有边界不清的肿块及压痛。计算机断层扫描显示,她的肠系膜有一个不规则的大分叶状肿块,位于盲肠内侧,并与多个小肠袢相关。术前鉴别诊断包括平滑肌肉瘤、淋巴瘤和胃肠道间质瘤。肠系膜肿块被切除,病理确诊为平滑肌肉瘤。该患者的肿瘤是肠系膜平滑肌肉瘤的典型病例,初次切除两年后出现肝转移复发。这类肿瘤通常在疾病晚期才出现症状,往往是在发生远处转移之后。肠系膜平滑肌肉瘤很罕见,报告发病率为1:350,000。