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先天性处女膜闭锁及其在新生儿期危及生命的后果。

Congenital imperforate hymen and its life-threatening consequences in the neonatal period.

作者信息

El-Messidi A, Fleming N A

机构信息

Department of Obstetrics and Gynecology, University of Ottawa, Ontario, Canada.

出版信息

J Pediatr Adolesc Gynecol. 2006 Apr;19(2):99-103. doi: 10.1016/j.jpag.2006.01.005.

DOI:10.1016/j.jpag.2006.01.005
PMID:16624697
Abstract

Imperforate hymen is most commonly an isolated finding and usually remains asymptomatic until puberty. Rarely, symptoms of imperforate hymen manifest antenatally as well as in the neonatal period, requiring surgical correction for life-threatening consequences. We report a 5-day-old infant with a large hydrometrocolpos causing severe renal compromise and abdominal ascites, successfully surgically treated in the neonatal period. Associated polydactyly suggested McKusick-Kaufman syndrome.

摘要

处女膜闭锁最常见的是一种孤立的发现,通常在青春期前无症状。很少有处女膜闭锁的症状在产前以及新生儿期就出现,因危及生命的后果而需要手术矫正。我们报告一例5天大的婴儿,患有巨大的阴道积血积脓,导致严重的肾功能损害和腹腔积液,在新生儿期成功接受了手术治疗。合并多指畸形提示麦库西克-考夫曼综合征。

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