Ma Y T, Ramachandra P, Spooner D
The Cancer Centre, Queen Elizabeth Hospital, Edgbaston, Birmingham B15 2TH, UK.
Br J Radiol. 2006 May;79(941):445-7. doi: 10.1259/bjr/61959899.
Extraspinal ependymomas are rare. The majority occur in the sacrococcygeal region. The subcutaneous variety accounts for approximately two thirds of cases, which are commonly misdiagnosed as a pilonidal cyst or sinus. Treatment is complete surgical resection. The role of coccygectomy is controversial. Adjuvant radiotherapy is of benefit to those with an incompletely excised tumour. Up to 20% metastasise, chiefly to the inguinal lymph glands, but pulmonary metastases are also reported. Palliative chemotherapy has not been shown to be of any benefit. Long term follow-up is important as metastases can occur up to 20 years after initial presentation. We report a 37-year-old woman with a subcutaneous sacrococcygeal ependymoma with iliac lymph nodal metastasis at presentation.
脊柱外室管膜瘤很罕见。大多数发生在骶尾区域。皮下型约占病例的三分之二，通常被误诊为藏毛窦或藏毛囊肿。治疗方法是完整的手术切除。尾骨切除术的作用存在争议。辅助放疗对肿瘤切除不完全的患者有益。高达20%的病例会发生转移，主要转移至腹股沟淋巴结，但也有肺转移的报道。姑息性化疗尚未显示有任何益处。长期随访很重要，因为转移可能在初次就诊后长达20年才出现。我们报告一名37岁女性，其骶尾皮下室管膜瘤在就诊时伴有髂淋巴结转移。
