Elloy Marianne Dawn, Cochrane Lesley Ann, Wyatt Michelle
Department of Paediatric Otolaryngology, Great Ormond Street Hospital for Children, London, UK.
J Craniofac Surg. 2006 Mar;17(2):272-4. doi: 10.1097/00001665-200603000-00012.
Pfeiffer syndrome is one of a group of craniosynostosis syndromes in which rare tracheal anomalies have been described. This group of patients have a poor prognosis, and mortality can be related to airway complications and respiratory distress. We report a case of type II Pfeiffer syndrome with tracheal cartilaginous sleeve and cricoid cartilage involvement. We discuss our strategy for the management of the airway of this patient.
法伊弗综合征是一组颅缝早闭综合征之一,其中已描述了罕见的气管异常。这组患者预后较差,死亡率可能与气道并发症和呼吸窘迫有关。我们报告一例伴有气管软骨套和环状软骨受累的II型法伊弗综合征病例。我们讨论了该患者气道管理的策略。