[Clinico-epidemiological aspects of hereditary neuromuscular diseases in the Krasnodar territory].

A study was made of the prevalence and clinical pleomorphism of neuromuscular diseases in the Krasnodar territory. The incidence of the diseases is 15.7 per 100,000 population (738 patients). Primary progressive myodystrophies are most prevalent (6.9 per 100,000 population). The humeroscapular and facial form (1.36 per 100,000 population) and Duchenne's form (1.15 per 100,000 population) occur less frequently. The remaining forms are an extreme rarity. Secondary amyotrophies occur more seldom (23.2%). Of these, there prevail Charcot-Marie amyotrophy (2.69 per 100,000 population). The myasthenia incidence constitutes 3.05 per 100,000 population. The myotonic syndromes were encountered in 12.3%. Of these, Thomsen's myotonia occurred most frequently (1.55 per 100,000 population).